ROP-like disorders

Familial exudative vitreoretinopathy

• Autosomal dominant (or X-linked)
• Asymmetrical, bilateral
• Abrupt cessation of peripheral retinal vessels at the equator
• Vitreous bands in the periphery
• Retinal ischaemia leads to fibrovascular membrane, retinal folds, macular ectopia (dragging of the retina temporally), retinal detachment,…