Paediatrics

Congenital Cataract

Lamellar cataracts are the most common form in congenital/infantile cataracts

  • Opacification within specific lens zones

Causes (and presenile cataract)

  • Isolated: usually autosomal dominant

  • Chromosomal:

    • Trisomies: Downs, Edwards, Patau

      • Downs is associated with ‘cerulean’ cataracts (small blue-white peripheral cortex opacities)
    • Turners

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